Pityriasis lichenoides et varioliformis acuta (Mucha-Habermann disease) is a distinctive eruption of unknown cause. A case of pityriasis lichenoides et varioliformis acuta, 24-year old male, was seen at dermatology department, St. Mary´s hospital, Catholic Medical College.
The eruption was polymorphic, consisting of pink papules. Some of the papules had a fine brown scale, while others became hemorrhagic and vesicular, leading to varioliform scarring on trunk and extremities except palms and soles without subjective symptoms.
Histopathological features were hyperkeratosis, parakeratosis, focal obliteration of the dermoepidermal junction by lymphocytes extending from the dermal papillae and invading the lower dermis, heavy perivascular lymphocytic infiltration, diapedesis of red blood cells into the corium and epid.rmis, and necrotic crust. The lesion was completely cleared with 10 mg of methotrexate by mouth twice a week for 4 weeks.
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